What is primary lymphedema? Primary lymphedema is caused by congenital abnormalities or functional decompensation of the lymphatic system. It can also be classified according to the age at initial examination. Congenital abnormalities can be detected at birth or within the first year of life, and may occur sporadically or in a familial pattern. Familial cases, such as Milroy's disease, are rare and are caused by autosomal single-gene abnormalities. Lymphedema usually develops between the ages of 1 and 35 for early-onset cases, and after the age of 35 for late-onset cases.
Primary lymphedema is more common in female patients, especially in early-onset cases, which often begin around the time of menarche. Symptoms may be associated with minor injuries.
Primary lymphedema can be categorized based on the type of lymphatic system abnormality: hypoplasia (underdevelopment) or hyperplasia (overdevelopment). However, it is relatively difficult to confirm lymphatic system abnormalities after birth.
Primary hypoplastic lymphedema can be divided into proximal or distal hypoplasia. Distal hypoplasia is more common, generally milder, often bilateral, and symptoms are limited to below the knee. Proximal lesions often cause severe symptoms and frequently involve the entire lower limb. Primary hyperplastic lymphedema refers to an increase in the number and size of lymphatics. This condition is rare, more common in males, and often familial. In these patients, the thoracic duct is often absent or abnormal.
What is primary lymphedema? The above is a detailed introduction by experts on what primary lymphedema is, hoping it will help you. If you have more questions, you can consult online with experts from Shanxi Yikang Peripheral Vascular Hospital. Finally, wishing you good health.
For more details, please visit the lymphedema special section of Shanxi Yikang Peripheral Vascular Hospital: http://www.sxykmgy.com/linbashuizhong/ or consult experts for free. Experts will provide detailed answers based on the specific circumstances of the patient.
If you reprint this article, please indicate the source as Shanxi Yikang Peripheral Vascular Hospital: http://www.sxykmgy.com/lbszby/21581.html